Test Code MISC2MAYOACRNS Acylcarnitines, Quantitative, Serum
Necessary Information
1. Patient's age is required.
2. Include family history, clinical condition (asymptomatic or acute episode), diet, and drug therapy information.
Specimen Required
Patient Preparation: Collect specimen just prior to a scheduled meal or feeding.
Collection Container/Tube:
Preferred: Red top
Acceptable: Serum gel
Submission Container/Tube: Plastic vial
Specimen Volume: 0.1 mL
Collection Instructions: Centrifuge and aliquot serum.
Secondary ID
60644Useful For
Diagnosis of fatty acid oxidation disorders and several organic acidurias in serum specimens
Evaluating treatment during follow-up of patients with fatty acid beta-oxidation disorders and several organic acidurias
Testing Algorithm
The following algorithms are available in Special Instructions:
Special Instructions
- Newborn Screening Follow-up for Isolated C4 Acylcarnitine Elevations (also applies to any plasma or serum C4 acylcarnitine elevations)
- Newborn Screening Follow-up for Elevations of C8, C6, and C10 Acylcarnitine Elevations (also applies to any plasma or serum C8, C6, and C10 acylcarnitine elevations)
- Newborn Screening Follow-up for Isolated C5 Acylcarnitines Elevations (also applies to any plasma or serum C5 acylcarnitine elevations)
Method Name
Flow Injection Analysis-Tandem Mass Spectrometry (FIA-MS/MS)
Reporting Name
Acylcarnitines, Quantitative, SSpecimen Type
SerumSpecimen Minimum Volume
0.04 mL
Specimen Stability Information
Specimen Type | Temperature | Time | Special Container |
---|---|---|---|
Serum | Frozen (preferred) | 60 days | |
Refrigerated | 21 days | ||
Ambient | 72 hours |
Reject Due To
Gross hemolysis | OK |
Gross lipemia | OK |
Gross icterus | OK |
Reference Values
≤7 days (nmol/mL) |
8 days-7 years (nmol/mL) |
≥8 years (nmol/mL) |
|
Acetylcarnitine, C2 |
2.14-15.89 |
2.00-27.57 |
2.00-17.83 |
Acrylylcarnitine, C3:1 |
<0.04 |
<0.05 |
<0.07 |
Propionylcarnitine, C3 |
<0.55 |
<1.78 |
<0.88 |
Formiminoglutamate, FIGLU |
<0.43 |
<0.08 |
<0.14 |
Iso-/Butyrylcarnitine, C4 |
<0.46 |
<1.06 |
<0.83 |
Tiglylcarnitine, C5:1 |
<0.05 |
<0.09 |
<0.11 |
Isovaleryl-/2-Methylbutyrylcarn C5 |
<0.38 |
<0.63 |
<0.51 |
3-OH-iso-/butyrylcarnitine, C4-OH |
<0.13 |
<0.51 |
<0.18 |
Hexenoylcarnitine, C6:1 |
<0.12 |
<0.10 |
<0.15 |
Hexanoylcarnitine, C6 |
<0.14 |
<0.23 |
<0.17 |
3-OH-isovalerylcarnitine, C5-OH |
<0.08 |
<0.12 |
<0.10 |
Benzoylcarnitine |
<0.13 |
<0.07 |
<0.10 |
Heptanoylcarnitine, C7 |
<0.05 |
<0.05 |
<0.06 |
3-OH-hexanoylcarnitine, C6-OH |
<0.08 |
<0.19 |
<0.09 |
Phenylacetylcarnitine |
<0.15 |
<0.22 |
<0.29 |
Salicylcarnitine |
<0.08 |
<0.09 |
<0.09 |
Octenoylcarnitine, C8:1 |
<0.48 |
<0.91 |
<0.88 |
Octanoylcarnitine, C8 |
<0.19 |
<0.45 |
<0.78 |
Malonylcarnitine, C3-DC |
<0.09 |
<0.14 |
<0.26 |
Decadienoylcarnitine, C10:2 |
<0.11 |
<0.12 |
<0.26 |
Decenoylcarnitine, C10:1 |
<0.25 |
<0.46 |
<0.47 |
Decanoylcarnitine, C10 |
<0.27 |
<0.91 |
<0.88 |
Methylmalonyl-/succinylcarn, C4-DC |
<0.05 |
<0.05 |
<0.05 |
3-OH-decenoylcarnitine, C10:1-OH |
<0.12 |
<0.12 |
<0.13 |
Glutarylcarnitine, C5-DC |
<0.06 |
<0.10 |
<0.11 |
Dodecenoylcarnitine, C12:1 |
<0.19 |
<0.37 |
<0.35 |
Dodecanoylcarnitine, C12 |
<0.18 |
<0.35 |
<0.26 |
3-Methylglutarylcarnitine, C6-DC |
<0.28 |
<0.21 |
<0.43 |
3-OH-dodecenoylcarnitine, C12:1-OH |
<0.11 |
<0.10 |
<0.13 |
3-OH-dodecanoylcarnitine, C12-OH |
<0.06 |
<0.09 |
<0.08 |
Tetradecadienoylcarnitine, C14:2 |
<0.09 |
<0.13 |
<0.18 |
Tetradecenoylcarnitine, C14:1 |
<0.16 |
<0.35 |
<0.24 |
Tetradecanoylcarnitine, C14 |
<0.11 |
<0.15 |
<0.12 |
Octanedioylcarnitine, C8-DC |
<0.25 |
<0.19 |
<0.19 |
3-OH-tetradecenoylcarnitine C14:1OH |
<0.06 |
<0.18 |
<0.13 |
3-OH-tetradecanoylcarnitine, C14-OH |
<0.04 |
<0.05 |
<0.08 |
Hexadecenoylcarnitine, C16:1 |
<0.15 |
<0.21 |
<0.10 |
Hexadecanoylcarnitine, C16 |
<0.36 |
<0.52 |
<0.23 |
3-OH-hexadecenoylcarnitine,C16:1-OH |
<0.78 |
<0.36 |
<0.06 |
3-OH-hexadecanoylcarnitine, C16-OH |
<0.10 |
<0.07 |
<0.06 |
Octadecadienoylcarnitine, C18:2 |
<0.12 |
<0.31 |
<0.24 |
Octadecenoylcarnitine, C18:1 |
<0.25 |
<0.45 |
<0.39 |
Octadecanoylcarnitine, C18 |
<0.10 |
<0.12 |
<0.14 |
Dodecanedioylcarnitine, C12-DC |
<0.10 |
<0.04 |
<0.04 |
3-OH-octadecadienoylcarn, C18:2-OH |
<0.04 |
<0.06 |
<0.06 |
3-OH-octadecenoylcarnitine C18:1-OH |
<0.03 |
<0.04 |
<0.06 |
3-OH-octadecanoylcarnitine, C18-OH |
<0.03 |
<0.05 |
<0.03 |
Day(s) and Time(s) Performed
Monday, Wednesday, Thursday, Friday; 8 a.m.
Performing Laboratory

Test Classification
This test was developed and its performance characteristics determined by Mayo Clinic in a manner consistent with CLIA requirements. This test has not been cleared or approved by the U.S. Food and Drug Administration.CPT Code Information
82017
LOINC Code Information
Test ID | Test Order Name | Order LOINC Value |
---|---|---|
ACRNS | Acylcarnitines, Quantitative, S | 43433-2 |
Result ID | Test Result Name | Result LOINC Value |
---|---|---|
92134 | Acetylcarnitine, C2 | 30191-1 |
92135 | Acrylylcarnitine, C3:1 | 43235-1 |
92136 | Propionylcarnitine, C3 | 30551-6 |
92137 | Formiminoglutamate, FIGLU | 79628-4 |
92138 | Iso-/Butyrylcarnitine, C4 | 35655-0 |
92139 | Tiglylcarnitine, C5:1 | 51416-6 |
92140 | Isovaleryl-/2-Methylbutyrylcarn C5 | 30531-8 |
92141 | 3-OH-iso-/butyrylcarnitine, C4-OH | 39000-5 |
92142 | Hexenoylcarnitine, C6:1 | 74540-6 |
92143 | Hexanoylcarnitine, C6 | 30358-6 |
92144 | 3-OH-isovalerylcarnitine, C5-OH | 39001-3 |
92145 | Benzoylcarnitine | 39615-0 |
92146 | Heptanoylcarnitine, C7 | 55871-8 |
92147 | 3-OH-hexanoylcarnitine, C6-OH | 30236-4 |
92148 | Phenylacetylcarnitine | 90237-9 |
92149 | Salicylcarnitine | 90238-7 |
92150 | Octenoylcarnitine, C8:1 | 30541-7 |
92151 | Octanoylcarnitine, C8 | 30540-9 |
92152 | Malonylcarnitine, C3-DC | 55940-1 |
92153 | Decadienoylcarnitine, C10:2 | 53471-9 |
92154 | Decenoylcarnitine, C10:1 | 30328-9 |
92155 | Decanoylcarnitine, C10 | 30327-1 |
92156 | Methylmalonyl-/succinylcarn, C4-DC | 51415-8 |
92157 | 3-OH-decenoylcarnitine, C10:1-OH | 82478-9 |
92158 | Glutarylcarnitine, C5-DC | 30349-5 |
92159 | Dodecenoylcarnitine, C12:1 | 30332-1 |
92160 | Dodecanoylcarnitine, C12 | 30331-3 |
92161 | 3-Methylglutarylcarnitine, C6-DC | 39002-1 |
92162 | 3-OH-dodecenoylcarnitine, C12:1-OH | 59195-8 |
92163 | 3-OH-dodecanoylcarnitine, C12-OH | 30233-1 |
92164 | Tetradecadienoylcarnitine, C14:2 | 30564-9 |
92165 | Tetradecenoylcarnitine, C14:1 | 30566-4 |
92166 | Tetradecanoylcarnitine, C14 | 30565-6 |
92167 | Octanedioylcarnitine, C8-DC | 39014-6 |
92168 | 3-OH-tetradecenoylcarnitine C14:1OH | 30190-3 |
92169 | 3-OH-tetradecanoylcarnitine, C14-OH | 30238-0 |
92170 | Hexadecenoylcarnitine, C16:1 | 30357-8 |
92171 | Hexadecanoylcarnitine, C16 | 30356-0 |
92172 | 3-OH-hexadecenoylcarnitine,C16:1-OH | 30235-6 |
92173 | 3-OH-hexadecanoylcarnitine, C16-OH | 30234-9 |
92174 | Octadecadienoylcarnitine, C18:2 | 30534-2 |
92175 | Octadecenoylcarnitine, C18:1 | 30542-5 |
92176 | Octadecanoylcarnitine, C18 | 30560-7 |
92177 | Dodecanedioylcarnitine, C12-DC | 55855-1 |
92178 | 3-OH-octadecadienoylcarn, C18:2-OH | 30237-2 |
92179 | 3-OH-octadecenoylcarnitine C18:1-OH | 30312-3 |
92180 | 3-OH-octadecanoylcarnitine, C18-OH | 35656-8 |
92181 | Comment (ACRNS) | 46252-3 |
Forms
If not ordering electronically, complete, print, and send an Inborn Errors of Metabolism Test Request (T798) with the specimen.